Method: GC-MS (Gas Chromatography/Mass Spectrometry) measuring organic acid metabolites in urine (CLIA 17D0919496); not cleared or approved by the FDA. Results in mmol/mol creatinine. Not a stand-alone diagnosis; should be interpreted in clinical context.
3-Methylglutaconic acid is tied to breaking down leucine and to cellular energy production, and is closely related to its companion marker 3-methylglutaric acid.



